| Names |
- Progressive hemifacial atrophy
- Idiopathic hemifacial atrophy
- Progressive facial hemiatrophy
Category: Skin |
| Prevalence |
476 cases in the US (Gupta 2016). Female/Male ratio: Unknown. |
| Age of Onset |
Onset typically occurs at age 10. |
| Description |
Progressive hemifacial atrophy, also called Parry Romberg Syndrome, predominantly affects the skin of the face and is believed to be autoimmune in nature, though the cause is still being researched. Typically, the skin deteriorates gradually over one side of the face, beginning with the upper jaw and the area extending from the nose to the corner of the lip, and then spreading to other parts of the face. In some cases, symptoms are not restricted to only one side of the face and may also occur in the trunk or limbs. Severe cases can spread to the muscles, bones, and cartilage. Patients can expect symptoms to progress over a period of 2 to 20 years, after which time progression plateaus. Treatments have so far been unsuccessful in stopping progression, but they do help manage associated discomfort. Cases that progress over longer periods of time and beginning at a younger age often lead to the most severe symptoms, resulting in facial distortions and nerve disorders.
Not confirmed as an autoimmune or autoinflammatory disease.
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| Resources |
Link to Clinical Trials
Link to PubMed |
| References |
Link to Mayo Clinic
Link to Cleveland Clinic
Link to Healthline
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Profile by: Leslie GreenProfile updated September 2024Charts generated Oct 12, 2024 at 12:54 PM ET |
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Progressive hemifacial atrophy sex breakdown
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Progressive hemifacial atrophy age breakdown
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